日本臨牀　別冊　血液症候群（第3版）II

出版社： 日本臨牀社
発行日： 2023-10-31
分野： 臨床医学：一般  >  雑誌
ISSN： 00471852
雑誌名：
特集： 血液症候群（第3版）II―その他の血液疾患を含めて―
電子書籍版： 2023-10-31 （第3版第1刷）
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目次

  • 特集　血液症候群（第3版）II
    　　　―その他の血液疾患を含めて―

    III．白血球(顆粒球)の異常(悪性腫瘍を除く)
    　１．類白血病反応
    　　（１）類白血病反応
    　　（２）一過性骨髄異常増殖症
    　２．好中球の異常
    　　（１）好中球増加症
    　　　　１）遺伝性好中球増加症
    　　　　２）慢性特発性好中球増加症
    　　　　３）偽性好中球増加症
    　　　　４）副腎皮質ステロイドによる好中球増加症
    　　　　５）妊娠性白血球増加症
    　　　　６）CSF産生腫瘍
    　　（２）好中球減少症
    　　　　１）無顆粒球症
    　　　　２）慢性特発性好中球減少症
    　　　　３）重症先天性好中球減少症
    　　　　４）Shwachman症候群
    　　　　５）同種免疫性好中球減少症
    　　　　６）自己免疫性好中球減少症
    　　　　(7）周期性好中球減少症
    　　（３）好中球機能異常症
    　　　　１）先天性好中球機能異常症
    　　　　　(1)Pelger-Huët anomaly
    　　　　　(2)MYH(9)異常症（May-Hegglin異常）
    　　　　　(3)Alder-Reilly anomaly
    　　　　　(4)チェディアック・東症候群
    　　　　　(5)ミエロペルオキシダーゼ欠損症
    　　　　　(6)好中球二次顆粒欠損症
    　　　　　(7)好中球アクチン機能異常症
    　　　　　(8)Job症候群
    　　　　　(9)なまけもの白血球症候群
    　　　　　(10)慢性肉芽腫症
    　　　　　(11)Jordans異常（中性脂肪蓄積心筋血管症を中心に）
    　　　　２）後天性好中球機能異常症
    　　　　　(1)偽Pelger-Huët核異常
    　　　　　(2)Dohle小体
    　３．好酸球の異常
    　　（１）好酸球増加症
    　　　　１）PIE症候群
    　　　　　(1)Löffler症候群
    　　　　　(2)遷延性肺好酸球(増加)症
    　　　　　(3)アレルギー性気管支肺アスペルギルス/真菌症（ABPA/M）
    　　　　　(4)好酸球性多発血管炎性肉芽腫症
    　　　　　　　（旧名称：アレルギー性肉芽腫性血管炎, Churg-Strauss 症候群
    　　　　　(5)多発血管炎性肉芽腫症
    　　　　　(6)結節性動脈周囲炎、結節性多発動脈炎
    　　　　２）特発性好酸球増加症候群
    　　　　３）好酸球性血管性浮腫
    　　　　４）好酸球性胃腸炎
    　　　　５）寄生虫感染による好酸球増加症
    　４．好塩基球の異常
    　　（１）好塩基球増加症
    　　（２）好塩基球減少症
    　５．単球の異常
    　　（１）単球増加症
    　　（２）単球性類白血病反応
    　　（３）単球減少症
    　　　　　１）大理石骨病
    　６．肥満細胞の異常
    　　（１）全身性肥満細胞症

    IV．リンパ球の異常
    　１．リンパ球増加症
    　　（１）移植後リンパ球増殖症
    　　（２）特発性顆粒リンパ球増加性リンパ増殖性疾患
    　　（３）性染色体連鎖リンパ球増加症
    　　（４）リンパ球性類白血病反応
    　２．リンパ球減少症
    　　（１）リンパ球減少症
    　　　　１）先天性リンパ球減少症
    　　　　２）後天性リンパ球減少症
    　　（２）特発性CD4リンパ球減少症
    　３．伝染性単核症
    　　（１）Epstein-Barr ウイルスによる伝染性単核球症
    　　（２）サイトメガロウイルスによる伝染性単核球症
    　４．リンパ球機能異常と類縁疾患
    　　（１）原発性免疫不全症候群
    　　　　１）乳児一過性低ガンマグロブリン血症
    　　　　２）X連鎖無ガンマグロブリン血症
    　　　　３）分類不能型免疫不全症
    　　　　４）免疫グロブリンクラススイッチ異常症(高IgM症候群)
    　　　　５）選択的IgA欠損症
    　　　　６）IgM単独(選択的)欠損症
    　　　　(7)）単独IgGサブクラス欠損症
    　　　　(8)）DiGeorge 症候群
    　　　　(9)）プリンヌクレオシド・ホスホリラーゼ欠損症
    　　　　10）ビオチン依存性カルボキシラーゼ欠損症
    　　　　11）複合免疫不全症(CID)
    　　　　　(1)重症複合免疫不全症
    　　　　　(2)アデノシン・デアミナーゼ欠損症
    　　　　　(3)細網異形成症
    　　　　12）MHCクラスI/II欠損症
    　　　　13）Ataxia-telangiectasia
    　　　　14）Wiskott-Aldrich症候群
    　　　　15）Bloom（ブルーム）症候群
    　　　　16）Good症候群(免疫不全症を伴う胸腺腫)
    　　　　1(7)）Job症候群 (高IgE症候群-反復感染症候群)
    　　　　1(8)）補体異常症
    　　（２）二次性免疫不全症候群
    　　　　１）後天性免疫不全症候群
    　　　　２）その他の二次性免疫不全症候群

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III 白血球 ( 顆粒球 ) の異常 ( 悪性腫瘍を除く )

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IV リンパ球の異常

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